Hydroa Vacciniforme- Uncommon photo-induced scarring disorder seen in early childhood and may resolve by adolescence or young adulthood; worse in spring/summer and in some cases may be associated with latent EBV infection; hydroa-vacciniforme- like skin changes with a specific type of EBV-associated lymphoma
- Presents with erythematous papules and plaques on sun-exposed sites within hours of sun exposure → evolve into hemorrhagic bullae with crusting → heal with varioliform scars
- Histology: early spongiosis, focal intraepidermal vesicles, keratinocyte degeneration, epidermal/upper dermal necrosis
- Treatment: refractory to treatment, photoprotection
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