Kaposiform Hemangioendothelioma

• Figure 2.17 A: Kaposiform hemangioendothelioma (in Kasabach-Merritt) (Reprint from Laxer RM, ed. The Hospital for Sick Children: Atlas of Pediatrics. Philadelphia, PA: Current Medicine; 2005) B: Port-wine stain (Reprint from Abel-Halim AW. Passing the USMLE. New York, NY: Springer; 2009) C: Glomangiomas (Courtesy of Dr. Michelle B. Bain)

  Usually onset before age 2
• Presents as vascular macules, plaques, nodules, or bulging indurated masses
• Associated with Kasabach–Merritt syndrome → consumptive coagulopathy with thrombocytopenia (platelet sequestration) and purpura; deepseated tumors (i.e., retroperitoneal) likely to cause above syndrome