How is it treated?

Surgical excision with careful margin control. Mohs micrographic surgery can be useful, but the tumor can be multifocal and local recurrences occur.

Hendi A, Brodland DG, Zitelli JA: Extramammary Paget’s disease: surgical treatment with Mohs micrographic surgery, J Am Acad Dermatol 51:767–773, 2004.