KP Atrophicans

• Group of disorders in children with faulty follicular keratinization followed by atrophy and scarring
  • KP atrophicans faciei: erythema with follicular spiny papules of eyebrows, cheeks, and scalp; involute and leave pitted atrophic scars; term ulerythema ophyrogenes if limited to lateral 1/3 of eyebrows, associated with Noonan syndrome
  • Atrophoderma vermiculata: pit-like atrophic scarring of follicles on face (“honeycomb” atrophy), associated with Rombo syndrome and Down syndrome