Presents as solitary or multiple deep nodules with rapid enlargement or ulceration; predilection for head, neck, or extremities
Histology: ranges from well-differentiated neoplasm with resemblance to leiomyoma to poorly differentiated neoplasm with liking to atypical fibroxanthoma; more cellular with atypia and mitoses than in leiomyoma
Prognosis excellent; dermal lesions rarely metastasize but subcutaneous lesions may (up to 30–40% of cases)